Table 2 Comparison of aortic dimension and WSS between MFS groups and healthy subjects

Age (y)

15.6 ± 4.5

15.6 ± 4.0

16.0 ± 2.6

Females (n)

3

8

12

BSA (m²)

1.6 ± 0.4

1.8 ± 0.3

1.6 ± 0.3

 Z-score Aortic Root**

4.4 ± 1.3

3.2 ± 1.4

0.5 ± 0.8

 Z-score STJ**

3.0 ± 0.9

1.2 ± 1.0

−0.3 ± 0.8

 Z-score AAo**

1.1 ± 0.7

−0.1 ± 0.8

−0.5 ± 0.6

 Z-score distal Arch*

0.8 ± 0.7

−0.1 ± 0.9

−0.2 ± 0.7

 Z-score Isthmus**

2.0 ± 0.7

0.6 ± 0.7

0.4 ± 0.5

 Z-score proximal DAo**

4.2 ± 1.1

1.2 ± 0.6

0.6 ± 0.7

 Δ diameter Root-AAo (%)**

30.9 ± 4.0

33.8 ± 7.0

19.0 ± 7.0

 Δ diameter Isthmus-pDAo (%)**

27.9 ± 9.1

10.4 ± 10.1

1.9 ± 5.7

 1. Inner pAAo*

0.69 ± 0.18

0.81 ± 0.09

0.86 ± 0.16

 2. Outer pAAo

0.59 ± 0.11

0.67 ± 0.11

0.73 ± 0.14

 3. Inner dAAo*

0.85 ± 0.18

0.97 ± 0.11

0.85 ± 0.15

 4. Outer dAAo

0.75 ± 0.14

0.87 ± 0.11

0.83 ± 0.14

 5. Inner Arch

0.83 ± 0.13

0.99 ± 0.13

0.91 ± 0.16

 6. Outer Arch

0.71 ± 0.09

0.80 ± 0.11

0.79 ± 0.14

 7. Inner pDAo*

0.58 ± 0.13

0.80 ± 0.14

0.87 ± 0.21

 8. Outer pDAo

0.76 ± 0.13

0.89 ± 0.10

0.86 ± 0.12

 9. Inner dDAo

0.75 ± 0.09

0.89 ± 0.16

0.89 ± 0.17

 10. Outer dDAo*

0.78 ± 0.05

0.99 ± 0.18

0.97 ± 0.16