Table 2 Characteristics of patients with Fontan circulation by thoracic duct tortuosity
Variable | None/mild (n = 119) | Moderate/severe (n = 50) | p-value |
|---|---|---|---|
Male | 78 (66%) | 33 (66%) | 1.00 |
Primary cardiac diagnosis | 0.05 | ||
Tricuspid atresia | 24 (20%) | 6 (12%) | |
HLHS | 39 (33%) | 18 (36%) | |
DILV | 10 (8%) | 6 (12%) | |
DORV | 25 (21%) | 3 (6%) | |
Unbalanced CAVC | 6 (5%) | 4 (8%) | |
Small right heart | 6 (5%) | 3 (6%) | |
Other | 9 (8%) | 10 (20%) | |
Heterotaxy syndrome | 1.00 | ||
Yes | 22 (19%) | 9 (18%) | |
No | 97 (82%) | 41 (82%) | |
Median age at Fontan, years | 2.7 (2.2, 3.6) | 3.0 (2.3, 3.7) | 0.23 |
Fontan type | 0.04 | ||
Lateral tunnel | 86 (72%) | 26 (52%) | |
Extracardiac | 25 (21%) | 17 (34%) | |
RA-PA | 7 (6%) | 5 (10%) | |
Other | 1 (1%) | 2 (4%) | |
Fontan revision | 1.00 | ||
Yes | 5 (4%) | 2 (4%) | |
No | 114 (96%) | 48 (96%) | |
Ventricular morphology | 0.08 | ||
Right | 57 (50%) | 20 (42%) | |
Left | 44 (38%) | 15 (31%) | |
Both | 14 (12%) | 13 (27%) | |
Median age at MRI, years | 17.1 (12.3, 24.5) | 15.2 (10.4, 22.6) | 0.27 |
BSA at MRI | 1.54 ± 0.42 | 1.46 ± 0.49 | 0.32 |