PA/IVS (n = 15) | LDAVC (n = 15) | |||||
---|---|---|---|---|---|---|
All | 1.5 V | 2 V | All | 1.5 V | 2 V | |
N | 15 | 10 | 5 | 15 | 1 | 14 |
Age at CMR (yrs) | 1.32 (0.37–12.63) | 3.27 (0.37–12.63) | 1.07 (0.47–1.32) | 1.04 (0.20–5.20) | 0.40 | 1.13 (0.20–5.20) |
Age at conversion surgery (yrs) | 1.34 (0.38–13.10) | 3.84 (0.38–13.10) | 1.10 (0.48–1.43) | 1.24 (0.22–5.20) | 0.46 | 1.30 (0.22–5.20) |
Female (n) | 5 | 3 | 2 | 11 | 0 | 11 |
Genetic syndrome (n) | 1 | 1 | 0 | 15 | 1 | 14 |
Body surface area (m2) | 0.50 (0.30–1.35) | 0.55 (0.30–1.35) | 0.46 (0.33–0.50) | 0.39 (0.25–0.68) | 0.31 | 0.40 (0.25–0.68) |
Circulation at CMR (n) | ||||||
Modified BTT/central shunt | 3 | 1 | 2 | 3 | 1 | 2 |
Pulmonary artery band | 0 | 0 | 0 | 8 | 0 | 8 |
Bidirectional Glenn | 6 | 6 | 0 | 2 | 0 | 2 |
Ductal stent | 5 | 2 | 3 | 0 | 0 | 0 |
Fontan | 1 | 1 | 0 | 0 | 0 | 0 |
Dual source of pulmonary blood flow (n) | 11 | 6 | 5 | 2 | 0 | 2 |
CMR parameters | ||||||
Heart rate (bpm) | 106 (76–135) | 104 (76–126) | 125 (101–135) | 110 (71–130) | 130 | 106 (71–125) |
RV EDV (ml/m2) | 34 (13–55) | 24 (13–40) | 46 (27–55) | 41 (15–102) | 15 | 43 (22–102) |
RV ESV (ml/m2) | 13 (6–27) | 13 (6–20) | 13 (10–27) | 14 (7–64) | 7 | 15 (8–64) |
RV stroke volume (ml/m2) | 19 (2–33) | 6 (2–31) | 30 (14–33) | 27 (8–55) | 8 | 28 (13–55) |
RV ejection fraction (%) | 54 (10–78) | 53 (10–78) | 54 (43–74) | 61(37–75) | 56 | 62 (37–75) |
RV mass (g/m2) | 10 (5–21) | 7 (5–15) | 12 (5–21) | 15 (5–33) | 5 | 16 (7–33) |
LV EDV (ml/m2) | 85 (51–166) | 85 (59–127) | 75 (51–166) | 97 (55–250) | 95 | 98 (55–250) |
LV ESV (ml/m2) | 36 (16–88) | 36 (21–61) | 28 (16–88) | 36 (23–123) | 42 | 35 (23–123) |
LV stroke volume (ml/m2) | 49 (27–78) | 50 (36–70) | 48 (27–78) | 60 (29–128) | 52 | 62 (29–128) |
LV ejection fraction (%) | 60 (44–73) | 59 (44–71) | 60 (47–73) | 60 (51–70) | 55 | 61 (51–70) |
RV:LV stroke volume ratio | 0.41 (0.04–0.70) | 0.17 (0.04–0.54) | 0.51 (0.26–0.70) | 0.45 (0.15–0.81) | 0.15 | 0.50 (0.21–0.81) |
TV:MV inflow ratio | 0.18 (0.004–0.51) | 0.18 (0.004–0.27) | 0.42 (0.12–0.51) | |||
TV anteroposterior diameter (cm) | 1.35 (0.44–1.70) | 0.98 (0.44–1.70) | 1.40 (1.18–1.62) | |||
TV lateral diameter (cm) | 1.23 (0.47–1.80) | 1.10 (0.47–1.80) | 1.60 (1.35–1.61) | |||
RV LGE present / LGE performed (n) | 4/11 | 2/7 | 2/4 | 0/10 | 0/1 | 0/9 |