Characteristic | Value |
---|---|
No of PAH patients | n = 34 |
Idiopathic PAH | n = 14 |
Familial PAH | n = 6 |
PAH and Collagen vascular disease | n = 5 |
PAH and HIV infection | n = 6 |
PAH and Porto pulmonary syndrome | n = 3 |
Age, yr | 54 ± 17 |
Male/female | 11/23 |
Functional status: | Â |
   NYHA II | n = 18 |
   NYHA III | n = 12 |
   NYHA IV | n = 4 |
   6 min walk test, m | 441 ± 109 |
Hemodynamic variables: | Â |
   Pra, mmHg | 7 ± 4.5 |
   sPap, mmHg | 74 ± 21 |
   dPap, mmHg | 29 ± 11 |
   mPap, mmHg | 45 ± 10 |
   Pcwp, mmHg | 6.9 ± 3.3 |
   SaO2, % | 95 ± 2 |
   SvO2, % | 63 ± 8 |
   Q-Fick, l/min | 4.7 ± 1.3 |
   CI, l·min-1·m-2 | 2.5 ± 0.6 |
   HR, min-1 | 81.5 ± 12 |
   SV-Fick, ml/beat | 58.8 ± 16 |
   PVR, dynes·s-1·cm-5 | 777 ± 402 |