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Table 3 Comparison between in patients with Miyoshi myopathy and age-matched health control subjects

From: Early detection of cardiac involvement in Miyoshi myopathy: 2D strain echocardiography and late gadolinium enhancement cardiovascular magnetic resonance

 

Patients with

MM (n = 5)

Control

(n = 5)

p-value

Age

43.8 ± 12.7

43.8 ± 12.7

1.0

Sex(Female)

2

2

1.0

SBP

126.8 ± 28

124.8 ± 18

0.883

DBP

81.6 ± 19

75.0 ± 10

0.527

HR

75.2 ± 14

69.8 ± 7.8

0.423

LVEDD (mm)

49.6 ± 5.9

49.2 ± 3.3

0.888

LVESD (mm)

32.0 ± 7.1

29.6 ± 3.2

0.518

Ejection Fraction (%)

59.6 ± 8.6

63.5 ± 3.8

0.379

E velocity (m/sec)

0.73 ± 0.20

0.85 ± 0.06

0.239

A velocity (m/sec)

0.58 ± 0.06

0.57 ± 0.05

0.777

E/A ratio (m/sec)

1.29 ± 0.46

1.51 ± 0.21

0.347

E' velocity (m/sec)

0.08 ± 0.02

0.09 ± 0.01

0.529

E/E' ratio

8.64 ± 0.29

9.61 ± 1.56

0.209

Global PSLS (%)

-18.8 ± 3.2

-24.4 ± 1.8

0.005

PSLS at long-axis view (%)

-18.2 ± 4.3

-24.1 ± 1.9

0.017

PSLS at 4-chamber view (%)

-19.1 ± 2.8

-22.9 ± 2.9

0.019

PSLS at 2-chamber view (%)

-19.3 ± 3.2

-24.4 ± 2.7

0.010

Segmental PSLS

   

Basal Anterior

-19.6 ± 4.3

-23.4 ± 1.7

0.102

   AS

-16.0 ± 2.1

-22.5 ± 1.1

<0.0001

   IS

-16.2 ± 2.5

-23.4 ± 1.2

<0.0001

   Inferior

-18.4 ± 6.2

-22.3 ± 1.6

0.213

   IL

-14.2 ± 1.9

-21.9 ± 2.9

0.162

   AL

-17.4 ± 6.1

-22.6 ± 2.6

0.106

Mid Anterior

-18.0 ± 4.8

-23.4 ± 2.3

0.038

   AS

--20.2 ± 3.3

-22.1 ± 2.2

0.248

   IS

-18.2 ± 2.2

-22.9 ± 2.2

0.003

   Inferior

-19.0 ± 4.4

-22.4 ± 2.4

0.137

   IL

-17.0 ± 5.8

-21.9 ± 1.7

0.109

   AL

-18.6 ± 5.6

-23.2 ± 2.8

0.164

Apical anterior

-20.0 ± 4.4

-22.9 ± 2.7

0.206

   septum

-23.4 ± 3.2

-23.1 ± 2.8

0.86

   Inferior

-22.8 ± 4.3

-22.7 ± 2.6

0.947

   lateral

-20.8 ± 4.5

-21.7 ± 2.2

0.684

Apical cap

-21.2 ± 3.7

-22.6 ± 2.5

0.463

  1. SBP = systolic blood pressure, DBP = diastolic blood pressure, HR = heart rate, LVEDD = left ventricular end-diastolic diameter, LVESD = left ventricular end-systolic diameter, E = peak transmitral flow velocity during early diastole, A = peak transmitral flow velocity during late diastole, E'= peak mitral annular velocity during early diastole, PSLS = peak systolic longitudinal strain, AS = anterior septum, IS = inferior septum, IL = inferior lateral, AL = anterior lateral.