Skip to main content

Table 4 The results of CMR in patients with Miyoshi myopathy

From: Early detection of cardiac involvement in Miyoshi myopathy: 2D strain echocardiography and late gadolinium enhancement cardiovascular magnetic resonance

 

#1

#2

#3

#4

#5

fibrosis

Mid anterior, mid anterolateral

Basal to mid inferolateral

No evidence of myocardial fibrosis

Basal to mid inferior, basal anteroseptal

septal side

LVEF (%)

53.7

53.8

53.7

41.4

59.7

Stroke volume (ml)

61.9

73.9

44.2

43.5-

44.3

Cardiac output (l/min)

4.3

6.4

2.9

3.04-

2.5 l

LVEDV (ml)

115.3

137.3

82.2

156.03

74.16

LVESV (ml)

53.4

64.5

38.1

91.49

29.9

LVEDWM (g)

80.1

169.8

47.9

112.89

49.56

  1. LVEF = left ventricular ejection fraction, LVEDV = left ventricular end-diastolic volume, LVESV = left ventricular end-systolic volume, LVEDWM = Left ventricular end-diastolic wall mass.