Gp 1 IPAH n = 28 | Gp 1 PAH-CTD n = 39 | Gp 2 PH-LHD n = 21 | Gp 3 RESP n = 29 | Gp 4 CTEPH n = 59 | |
---|---|---|---|---|---|
Demographics and RHC | |||||
Age (yrs) | 53 ± 17¶, +, §, ƒ | 67 ± 9# | 74 ± 9# | 67 ± 12# | 64 ± 14# |
mPAP (mmHg) | 54 ± 13¶, +, § | 40 ± 13#, ƒ | 35 ± 8#, ƒ | 39 ± 8#, ƒ | 49 ± 10¶, +, § |
PCWP (mmHg) | 11 ± 3+ | 11 ± 4+ | 21 ± 4#, ¶, §, ƒ | 12 ± 4+ | 12 ± 5+ |
mRAP (mmHg) | 11 ± 5 | 9 ± 5+ | 14 ± 5¶, § | 9 ± 4+ | 12 ± 6 |
CO (L.min) | 4.6 ± 1.4+ | 5.2 ± 1.6 | 6.2 ± 1.7#, ƒ | 5.3 ± 1.3 | 4.8 ± 1.5+ |
CI (L.min.m-2) | 2.5 ± 0.7¶, + | 3.1 ± 0.7#, ƒ | 3.4 ± 0.8#, ƒ | 3.0 ± 0.6 | 2.5 ± 0.7¶, + |
PVR (dyn.s.cm-5) | 876 ± 439¶, +, § | 484 ± 337#, ƒ, + | 183 ± 87¶, #, ƒ, | 428 ± 206#, ƒ | 736 ± 373¶, +, § |
CMR | |||||
RVEDVI (ml/m2) | 119 ± 47 | 82 ± 27+, ƒ | 91 ± 38¶ | 96 ± 33 | 108 ± 41¶ |
VMI (ratio) | 1.0 ± 0.4¶, +, § | 0.6 ± 0.4#, ƒ, + | 0.3 ± 0.1#, ƒ, ¶ | 0.6 ± 0.2#, ƒ | 0.8 ± 3.1¶, +, § |
RV mass index (g/m2) | 50 ± 19¶, +, § | 27 ± 14#, ƒ | 22 ± 11#, ƒ | 32 ± 11#, ƒ | 43 ± 16¶, +, § |
Late gadolinium enhancement ratio and % | 21/22 (95%)+ | 20/28 (77%) | 4/15 (27%)#, ƒ | 19/20 (95%) | 38/39 (97%)+ |
RVEF (%) | 23 ± 15 | 32 ± 16 ƒ | 32 ± 10 ƒ | 24 ± 15 | 21 ± 12¶, + |
RVSVI (ml/m2) | 26 ± 21 | 24 ± 14 | 29 ± 13 | 22 ± 13 | 21 ± 11 |
TAPSE (cm) | 1.5 ± 0.5 | 1.6 ± 0.7 | 2.0 ± 0.6§, ƒ | 1.4 ± 0.7+ | 1.2 ± 0.5+ |
sEI (ratio) | 2.2 ± 0.6¶, +, §, ƒ | 1.4 ± 0.4# | 1.2 ± 0.2#, ƒ | 1.3 ± 0.3#, ƒ | 1.6 ± 0.5#,+, § |
dEI (ratio) | 1.5 ± 0.4¶, +, §, ƒ | 1.3 ± 0.2# | 1.2 ± 0.2# | 1.1 ± 0.1# | 1.3 ± 0.3# |
Average velocity (cm/s) | 7.0 ± 3.0 | 10.0 ± 3.7 ƒ | 9.1 ± 3.4 | 7.4 ± 3.4 | 5.9 ± 2.5¶ |
Retrograde flow (L/min/m2) | 0.5 ± 0.3 | 0.4 ± 0.3 | 0.5 ± 0.3 | 0.4 ± 0.2 | 0.5 ± 0.3 |
PA relative area change (%) | 6 ± 5+ | 9 ± 6 | 13 ± 10#, ƒ | 8.2 ± 6.0 | 6.5 ± 4.0+ |
Systolic PA area (cm2) | 9.4 ± 1.8 | 9.0 ± 2.1 | 9.0 ± 2.2 | 9.1 ± 1.9 | 9.9 ± 2.2 |
Diastolic PA area (cm2) | 8.9 ± 1.8 | 8.1 ± 2.1 | 7.8 ± 2.0 | 8.2 ± 2.0 | 9.2 ± 2.0 |