A case of a 3-month-old female with pulmonary sequestration spectrum. (A, B) Axial ECG-gated spin-echo T1WI at diaphragm level (A): an anomalous arterial supply from descending aorta (arrow). (B), the artery courses serpiginously (arrowhead) supplying the basal segments of the left lower lung. (C) Contrast-enhanced 3D MR angiography: An anomalous arterial supply from aorta (arrow) to the left lower lung (arrowhead). The course and branching pattern in the basal segments was identical to those confirmed by catheter angiography (D). (E) DCE-MRI after bolus injection. Two ROIs were chosen on left upper lung and left lower lung. (F) SI-time curve of left low lung showed a delayed bolus-arrival as compared to curve of left upper lung. (G) Tc-99M-MAA pulmonary perfusion scintigraphy (posterior-anterior view) shows decreased perfusion over the left lower zone. (H) rPBV map of whole lungs calculated from DCE-MRI. There was no obvious flow deficit in rPBV map. (I) rPBViw map of the whole lungs. It is similar to Figure (H) except that inflow-weighted analysis was calculated instead of rPBV analysis. rPBViw map showed a flow deficit in the left lower lung.