Age at death (yrs)
|
22.7 ± 10.8
|
Male (%)
|
71%
|
BMI (kg/m2)
|
25.6 ± 5.8
|
Time to autopsy (hrs)
|
56.1 ± 17.2
|
Family history of sudden death, n (%)
|
2 (12)
|
Cause of death, n (%)
|
17 (100)
|
1) Primary Cardiac
|
8 (47)
|
• ARVC
|
4 (24)
|
• CAD
|
2 (12)
|
• HCM
|
1 (6)
|
• Myocarditis
|
1 (6)
|
2) Neurological
|
2 (12)
|
• GBM
|
1 (6)
|
• SUDEP (Alagille syndrome)
|
1 (6)
|
3) Vascular
|
2 (12)
|
• Pulmonary embolus
|
1 (6)
|
• Aortic dissection
|
1 (6)
|
4) Unexplained
|
5 (35)
|
- NB: BMI = body mass index; ARVC = arrhythmogenic right ventricular cardiomyopathy; CAD = coronary artery disease; HCM = hypertrophic cardiomyopathy; GBM = glioblastoma multiforme; SUDEP = sudden unexpected death in epilepsy.