Table 1 Demographic and clinical data in the BHLHS group

Initial anatomy

Multiple left heart obstructions

19 (86%)

Critical aortic stenosis

3 (14%)

Female

7 (32%)

In utero aortic valvuloplasty

9 (40%)

Age at CMR (mo)

39 (0–82)

Body surface area (m²)

0.59 (0.22-0.72)

Circulation at the time of CMR

Prostaglandin infusion

3 (13%)

Norwood stage 1 palliation

2 (9%)

Hybrid stage 1 palliation

1 (5%)

Bidirectional Glenn shunt

15 (68%)

Total cavopulmonary connection

1 (5%)

Prior procedure to increase left heart flow

17 (77%)

Dual sources of pulmonary blood flow

13

Restriction of the atrial septal defect

16

CMR parameters

Heart rate (beats/min)

110 (89–150)

LV EDV (ml/m²)

57 (21–88)

LV ESV (ml/m²)

21 (10–49)

LV stroke volume (ml/m²)

31 (4–60)

LV ejection fraction (%)

61 (20–79)

RV EDV (ml/m²)

82 (52–132)

RV ESV (ml/m²)

39 (22–82)

RV stroke volume (ml/m²)

42 (17–65)

RV ejection fraction (%)

54 (27–66)

LV-to-RV stroke volume ratio

0.8 (0.06-1.7)

MV-to-TV inflow ratio

1.0 (0.2-3.0)

LGE pattern consistent with EFE

16 (73%)

LA pressure (mm Hg)

14 (5–16)

LV ED pressure (mm Hg)

12 (8–22)

Biventricular procedure CPB time (min)

149 (92–239)

Biventricular procedure LOS (days)

25 (7–156)