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Table 1 Demographic, hemodynamic, and cardiac magnetic resonance data for all subjects

From: Non-invasive determination by cardiovascular magnetic resonance of right ventricular-vascular coupling in children and adolescents with pulmonary hypertension

Subject demographics (n = 17)

Age

11.0 years (range 0.25–23.0)

Male gender

9/17

BSA (m2)

1.2 ± 0.5

Pulmonary Hypertension Classificationa

 

 1. Pulmonary arterial hypertension

15

  1.1 Idiopathic

5

  1.3 Drug and Toxin-induced (anthracycline)

1

  1.4.1 Connective tissue disorder (Overlap syndome)

1

  1.4.3 Portal hypertension

1

  1.4.4 Congenital heart disease

6

  Atrial septal defect

4

  Atrioventricular septal defect

1

  Partial anomalous pulmonary venous return

1

  1.4.5 Pulmonary hypertension from schistosomiasis

1

 3. Pulmonary hypertension due to lung disease

2

World Health Organization Functional Classification

 

 WHO-FC I

2

 WHO-FC II

8

 WHO-FC III

4

 WHO-FC IV

1

Pulmonary artery pressure

 

 Systolic pulmonary artery pressure (mmHg)

54.5 (20.6)

 Diastolic pulmonary artery pressure (mmHg)

25.4 (11.7)

 Mean pulmonary artery pressure (mmHg)

35 (15)

Pulmonary capillary wedge pressure (mmHg)

10.8 (3.2)

Pulmonary vascular resistance index (Woods unit x m2)

8.5 (7.8)

Cardiac output indexed (L/min/m2)

4.8 (1.5)

Right ventricular volume

 

 End-diastole (ml/m2)

118.4 (51.1)

 End-systole (ml/m2)

70.9 (42.9)

Right ventricular ejection fraction (%)

46.6 (9.7)

Right ventricular stroke volume indexed (ml/m2)

54.4 (12.7)

Ea (mmHg/ml/m2)

0.49 (0.26)

Emax (mmHg/ml/m2)

0.56 (0.18)

VVCRs

1.79 (0.34)

VVCRm

1.29 (0.72)

  1. aPulmonary hypertension classification based on 5th World Symposium in Nice, France in 2013 from Simommeau G et al. Updated clinical classification of pulmonary hypertension. JACC 2013:62:D34-41