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Table 2 Ventricular volumes, function and masses of PRKAG2 mutation carriers compared to age, gender and body surface area standardized reference values

From: Cardiovascular magnetic resonance findings in patients with PRKAG2 gene mutations

  All
  (n = 6)
  Value z-scorea
Left ventricle
 End-diastolic volume, ml 163 (116–180)  
 End-diastolic volume index, ml/m2 90 (82–100) 0.6 (-0.1–1.6)
 End-systolic volume, ml 63 (38–72)  
 End-systolic volume index, ml/m2 34 (28–42) 0.9 (-1.0–2.2)
 Stroke volume, ml 99 (78–109)  
 Stroke volume index, ml/m2 57 (52–59) 0.3 (-0.3–1.0)
 Cardiac output, l/min 5.9 (4.8–8.2)  
 Cardiac output index, l/(minam2) 3.5 (3.1–4.4)  
 LVEF, % 62 (58–67) −0.3 (-1.5–1.5)
 Mass, g 137 (96–335)  
 Mass index, g/m2 78 (68–203) 2.1 (-0.1–18.8)
Right ventricle
 End-diastolic volume, ml 167 (124–189)  
 End-diastolic volume index, ml/m2 95 (75–102) 0.3 (-1.0–0.9)
 End-systolic volume, ml 68 (38–83)  
 End-systolic volume index, ml/m2 39 (23–45) 0.2 (-1.3–1.3)
 Stroke volume, ml 99 (78–106)  
 Stroke volume index, ml/m2 56 (52–59) 0.2 (-0.2–0.7)
 Cardiac output, l/min 5.8 (4.9–8.2)  
 Cardiac output index, l/(minam2) 3.5 (3.1–4.4)  
 RVEF, % 59 (56–69) 0.1 (-1.1–1.3)
  1. Values are median (range)
  2. Abbreviations: LVEF left ventricular ejection fraction, RVEF right ventricular ejection fraction
  3. aZ-scores were calculated using the normal reference values for adults by Maceira A. et al. [30] and children by Buechel E. et al. [31]