Cardiovascular magnetic resonance findings in patients with PRKAG2 gene mutations

Table 3 Summary of ventricular wall thickness compared to normal reference values and late gadolinium enhancement of PRKAG2 mutation carriers

	All
	(n = 6)
	Value	z-score^a
Left ventricle
Left ventricular hypertrophy^b	6 (100)
Maximal wall thickness, mm	13 (11–37)	3.2 (2.3–19.0)
LGE presence	2 (33)
LGE extent, % left ventricular volume^c	17 (11–22)
Right ventricle
Free wall thickness, mm	5 (2–6)
LGE presence	0 (0)

Values are median (range) or n (%)
Abbreviation: LGE late gadolinium enhancement
^aStandardized wall thickness (z-score), see Statistics section
^bLeft ventricular hypertrophy was defined as > 2 z-score wall thickening in one or more myocardial segments
^cOnly two patients had LGE

ISSN: 1532-429X