Table 1 Demographics

Age (years)

24.5 ± 3.9 (range 18–30)

13.4 ± 4.7 (range 8–27)

Male Gender (%)

100 %

100 %

Height (cm)

182 ± 8

144 ± 15

Weight (kg)

76 ± 9

51 ± 16

BSA^b (m²)

2.0 ± 0.2

1.4 ± 0.3

BMI^c (kg/m²)

23.0 ± 1.5

24.1 ± 6.3

Heart Rate (bpm)

66 ± 4

94 ± 14

Ambulatory (%)

11 (100 %)

7 (22.6 %)

Ventilatory support (%)

0 %

7 (22.6 %)

 Caucasian

8 (72.7 %)

27 (87.1 %)

 African American

1 (9.1 %)

2 (6.5 %)

 Asian

1 (9.1 %)

2 (6.5 %)

 Other

0

0

 Mixed

1 (9.1 %)

0

Hispanic/Latino

1 (9.1 %)

3 (9.7 %)

 ACEi^e

0 %

14 (45.2 %)

 ARB^f

0 %

5 (16.1 %)

 β-blocker

0 %

10 (32.3 %)

 Corticosteroids

0 %

21 (67.7 %)

 Corticosteroid duration (years)

0

3.7 ± 3.2