Table 2 Results from CMR and echocardiography
| Patients (n = 31) | Controls (n = 15) | p | |
|---|---|---|---|
|
CMR Ventricular volumetry and pulmonary flow | |||
| RV enddiastolic volume [ml/m2] | 148 ± 40 | 93 ± 13 | <0.001 |
| RV endsystolic volume [ml/m2] | 75 ± 23 | 43 ± 8 | <0.001 |
| RV muscle mass [g/m2] | 39.4 ± 9.4 | n.a. | n.a. |
| RV ejection fraction [%] | 50 ± 5 | 53 ± 3 | <0.05 |
| LV enddiastolic volume [ml/m2] | 91 ± 12 | 89 ± 11 | 0.50 |
| LV endsystolic volume [ml/m2] | 41 ± 8 | 36 ± 6 | <0.05 |
| LV muscle mass [g/m2] | 46 ± 7 | 49 ± 9 | 0.29 |
| LV ejection fraction [%] | 55 ± 6 | 59 ± 4 | <0.01 |
| Pulmonary regurgitation [%] | 33 ± 16 | n.a. | n.a. |
| Z-Scores | |||
| RV enddiastolic volume | 3.42 (1.52–5.29) | −0.11 (−1.17–0.68) | <0.001 |
| RV endsystolic volume | 3.65 (1.52–4.51) | −0.05 (−0.33–0.98) | <0.001 |
| RV ejection fraction | −1.52 (−2.23– −0.69) | −1.04 (−1.29– −0.39) | <0.05 |
| LV enddiastolic volume | 0.62 ( −0.10–1.36) | 0.41 (−0.55–1.59) | 0.60 |
| LV endsystolic volume | 1.57 (−0.75–2.30) | 1.08 (−0.31–1.65) | <0.05 |
| LV muscle mass | −1.89 (−2.90– −0.94) | −0.96 (−2.43–0.36) | 0.24 |
| LV ejection fraction | −1.29 (−2.51– −0.80) | −0.32 (−1.41–0.41) | <0.01 |
| Echocardiography | |||
| RVSP [mmHg], n = 19 | 44 ± 15 | n.a. | n.a. |
| RVOT-gradient [mmHg], n = 29 | 32 ± 18 | n.a. | n.a. |
| TAPSE [mm], n = 19 | 16.5 ± 3.5 | n.a. | n.a. |
| Grade of tricuspid insufficiency [n (%)] | n.a. | n.a. | |
|
Trivial Mild |
17 (55 %) 14 (45 %) | ||