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Table 3 Glucocorticoid and cardiac medications and respiratory data for DMD subjects at time of CMR

From: Native T1 values identify myocardial changes and stratify disease severity in patients with Duchenne muscular dystrophy

DMD Subject

Glucocorticoid/ Cardiac Medications

FVC%

FEV1%

Nighttime support

Restrictive lung disease

1

Deflazacort

76 %

83 %

None

None

2

Prednisone, Lisinopril

54 %

44 %

None

Mild to moderate

3

Lisinopril

57 %

58 %

BiPAP

Mild

4

Lisinopril

55 %

65 %

None

Mild

5

Prednisone

116 %

115 %

None

None

6

Prednisone

27 %

32 %

BiPAP

Severe

7

Deflazacort

61 %

67 %

BiPAP

Moderate

8

Prednisone, Perindopril

55 %

59 %

None

Moderate

9

Prednisone, Lisinopril

57 %

54 %

None

Mild to moderate

10

Prednisolone

72 %

71 %

None

Mild

11

None

79 %

61 %

None

Mild

12

Prednisone, Perindopril

60 %

67 %

None

Mild to moderate

13

Deflazacort

121 %

111 %

None

None

14

Prednisone

92 %

92 %

None

None

15

Prednisolone

102 %

106 %

None

None

16

Prednisone, Lisinopril

58 %

67 %

BiPAP

Mild to moderate

17

Prednisolone

94 %

105 %

None

None

18

Prednisone, Perindopril

74 %

86 %

BiPAP

Mild

19

Deflazacort, Lisinopril

104 %

93 %

None

None

20

Prednisone, Lisinopril

46 %

50 %

BiPAP

Moderate to severe

  1. DMD Duchenne muscular dystrophy, FVC functional vital capacity, FEV forced exhaled volume