From: Increased extracellular volume in the liver of pediatric Fontan patients
 | Control n = 44 | BCPC n = 20 | Fontan n = 62 | p value BCPC vs control | p value Fontan vs control | p value Fontan vs BCPC | SLV Fontan. n = 34 | SRV Fontan n = 21 | p value SRV vs SLV |
---|---|---|---|---|---|---|---|---|---|
VEDVi (mL/m2) | 93 ± 13 | 135 ± 30 | 127 ± 41 | < 0.001* | < 0.001* | 0.4* | 119 ± 35 | 144 ± 49 | 0.03 |
VESVi (mL/m2) | 39 ± 7 | 76 ± 22 | 72 ± 31 | < 0.001* | < 0.001* | 0.5* | 64 ± 22 | 88 ± 40 | 0.05 |
VSVi (mL/m2) | 54 ± 8.9 | 59.1 ± 14.3 | 55.4 ± 16.3 | 0.2* | 0.6* | 0.3* | 55.7 ± 19.0 | 56.3 ± 12.3 | 0.9 |
Vmass (g/m2) | 55 ± 12 | 59 ± 15 | 57 ± 9 | 0.3* | 0.5* | 0.4* | 59 ± 10 | 53 ± 10 | 0.02 |
VEF (%) | 58 ± 5 | 44 ± 7 | 45 ± 8 | < 0.001* | < 0.001* | 0.7* | 47 ± 8 | 40 ± 8 | 0.009 |
Vmass / VEDV (g/mL) | – | 78 ± 19 | 71 ± 21 | – | – | 0.1 | 70 ± 20 | 76 ± 25 | 0.3 |
AAO (L/min/m2) | – | 4.2 ± 1.4 | 3.3 ± 0.7 | – | – | 0.01 | 3.2 ± 0.6 | 3.4 ± 0.9 | 0.4 |
APC (L/min/m2) | – | 1.2 ± 0.7 | 0.7 ± 0.5 | – | – | 0.004 | 0.6 ± 0.4 | 0.7 ± 0.5 | 0.7 |
Qp/Qs | – | 1.2 ± 0.4 | 1.1 ± 0.2 | – | – | 0.5 | 1.1 ± 0.2 | 1.1 ± 0.1 | 0.5 |
Hepatic native T1 (ms) | 604 ± 54 | 645 ± 43 | 762 ± 64 | < 0.001* | < 0.001* | 0.04* | 748 ± 51 | 780 ± 78 | 0.07 |
Hepatic ECV (%) n = 50 (with Gadobuturol) | – | 36.4 ± 4.8 n = 17 | 41.4 ± 4.8 n = 33 |  |  | 0.02 | 40.2 ± 4.2 | 43.1 ± 4.7 | 0.1 |