Overall (n = 493) | No endpoint (n = 470) | Endpoint (n = 23) | p-value | |
---|---|---|---|---|
HCM Risk-SCD | 0.018 | |||
Low risk, n (%) | 362 (73.4%) | 351 (74.7%) | 11 (47.8%) | – |
Intermediate risk, n (%) | 66 (13.4%) | 59 (12.6%) | 7 (30.4%) | – |
High risk, n (%) | 65 (13.2%) | 60 (12.8%) | 5 (21.7%) | – |
Risk at 5-years (%) | 2.5 (1.7–4.1) | 2.4 (1.7–4.0) | 4.2 (2.4–6.0) | 0.003 |
ACCF/AHA | 0.075 | |||
ICD not recommended, n (%) | 281 (57.0%) | 273 (58.1%) | 8 (34.8%) | – |
ICD can be useful, n (%) | 68 (13.8%) | 62 (13.2%) | 6 (26.1%) | – |
ICD reasonable, n (%) | 144 (29.2%) | 135 (28.7%) | 9 (39.1%) | – |
LGE classification | < 0.001 | |||
0%, n (%) | 102 (20.7%) | 102 (21.7%) | 0 (0%) | – |
0.1–10.0%, n (%) | 285 (57.8%) | 279 (59.4%) | 6 (26.1%) | – |
10.1–19.9%, n (%) | 63 (12.8%) | 55 (11.7%) | 8 (34.8%) | – |
≥ 20%, n (%) | 43 (8.7%) | 34 (7.2%) | 9 (39.1%) | – |