Original Task Force Criteria | Revised Task Force Criteria |
---|---|
A | |
I. Global or regional dysfunction and structural alterations; Imaging | |
Major | Major |
-Severe dilatation and reduction of RV ejection fraction with no LV impairment -Localized RV aneurysms -Severe segmental dilatation of the RV | By 2D echo: Regional RV akinesia, dyskinesia or aneurysm and 1 of the following (end diastole and corrected for body size (Parasternal long axis /BSA)): - Parasternal long axis RVOT > 32 mm Parasternal long axis /BSA > 19 mm/m2 - Parasternal short axis RVOT > 36 mm Parasternal short axis /BSA > 21 mm/m2 -Fractional area change < 33% By CMR: Regional RV akinesia or dyskinesia or dyssynchrounous RV contraction and 1 of the following: -Ratio of RV EDV to BSA > 110 ml/m2 (male) or > 100 ml/m2 (female) -RV ejection fraction < 40% |
Minor | Minor |
-Mild global RV dilatation and/or ejection fraction reduction with normal LV -Mild segmental dilatation of the RV -Regional RV hypokinesis | By 2D echo: Regional RV akinesia or dyskinesia and 1 of the following (end diastole and corrected for body size (Parasternal long axis /BSA)) -Parasternal long axis RVOT > 29 to < 32 mm Parasternal long axis /BSA > 16 to < 19 mm/m2 -Parasternal short axis RVOT > 32 to 36 mm Parasternal short axis /BSA > 18 to < 21 mm/m2 -RV Fractional area change > 33% to < 40% By MRI: Regional RV akinesia or dyskinesia or dyssynchrounous RV contraction and 1 of the following: -Ratio of RV EDV to BSA > 100 to < 110 ml/m2 (male) or > 90 to < 100 ml/m2 (female) -RV ejection fraction > 40% to < 45% |
B | |
V. Arrhythmias | |
Major | Major |
-Non-sustained or sustained ventricular tachycardia of left bundle-branch morphology with superior axis (negative or indeterminate QRS in leads II, III, and aVF and positive in lead aVL) | |
Minor | Minor |
-Left bundle-branch block-type ventricular tachycardia (sustained and non-sustained) -Frequent ventricular extra-systoles (1000 per 24 h) | -Non-sustained or sustained ventricular tachycardia of RV outflow configuration, left bundle-branch block morphology with inferior axis (positive QRS in leads II, III, and aVF and negative in lead aVL) or of unknown axis - > 500 ventricular extra-systoles per 24 h |
C | |
VI. Family history | |
Major | Major |
-Familial disease confirmed at necropsy or surgery | -ARVC confirmed in a first-degree relative who meets current Task Force criteria -ARVC confirmed pathologically at autopsy or surgery in a first-degree relative -Identification of a pathogenic mutation categorized as associated or probably associated with ARVC in the patient |
Minor | Minor |
-Family history of premature sudden death (35 years of age) due to suspected ARVC -Familial history (clinical diagnosis based on present criteria) | -History of ARVC in a first-degree relative in whom it is not possible or practical to determine whether the family member meets current Task Force criteria -Premature sudden death (35 years of age) due to suspected ARVC in a first-degree relative -ARVC confirmed pathologically or by current Task Force Criteria in second-degree relative |