Table 2 Baseline Patient Characteristics and Index CMR Characteristic
First Degree Relative with ARVC | First Degree Relative with premature death | Ventricular Tachycardia | Ventricular Extra-systoles | P value Family History vs Arrhythmia Group | |
|---|---|---|---|---|---|
n (%) | 16 (33.3%) | 8 (16.7%) | 13 (27.1%) | 11 (22.9%) | |
Age, years | 41.1 +/− 18.9 | 40.3 +/− 19.3 | 49.3 +/−13.1 | 55.4 +/− 9.2 | 0.015 |
Sex, Female, n (%) | 11 (68.8%) | 4 (50%) | 6 (46.1%) | 6 (54.5%) | 0.561 |
Treatment, n (%) | |||||
Beta Blockers | 0 | 0 | 2 (15.4%) | 2 (18.2%) | 0.109 |
Calcium Channel Blockers | 0 | 0 | 1 (7.7%) | 0 | 1.000 |
Electrical Ablation, n (%) | 0 | 0 | 3 (23.1%) | 0 | 0.234 |
Pathogenic mutation associated with ARVC, n (%) | |||||
-PKP2 | 4 (25%) | 0 | 0 | 0 | 0.109 |
Major Criteria from Another Category, n (%) | 16 (100%) | 0 | 13 (100%) | 0 | 0.556 |
Minor Criteria from Another Category, n (%) | 0 | 8 (100%) | 0 | 11 (100%) | 0.556 |
Index CMR | |||||
RV Dilatation, n (%) | 4 (25%) | 4 (50%) | 6 (46.2%) | 4 (36.6%) | 0.7661 |
RV Dyskinesia, n (%) | 12 (75%) | 4 (50%) | 7 (53.8%) | 7 (63.4%) | 0.7661 |
2010 Major Imaging, n (%) | 1 (6.3%) | 2 (25%) | 1 (7.7%) | 2 (18.2%) | 1.000 |
2010 Minor Imaging, n (%) | 15 (93.7%) | 6 (75%) | 12 (92.3%) | 9 (81.8%) | 1.000 |