Parameter | BAV (n = 49) | CTD (n = 50) | p value |
---|---|---|---|
Age at first CMR (years) | 23.0 ± 11 | 20.6 ± 12 | 0.30 |
Male gender | 36 (73%) | 32 (64%) | 0.26 |
Type of BAV | N/A | N/A | |
Left–right | 22 (45%) | ||
Right-non | 11 (22%) | ||
Left-non | 1 (2%) | ||
Unicuspid | 15 (31%) | ||
Type of CTD | N/A | N/A | |
Marfan syndrome | 26 (52%) | ||
Nonspecific CTD | 14 (28%) | ||
Loeys-Dietz syndrome | 7 (14%) | ||
Ehlers-Danlos syndrome | 3 (6%) | ||
Aortic regurgitation | < 0.001 | ||
None/trivial | 12 (25%) | 47 (94%) | |
Mild | 30 (63%) | 3 (6%) | |
Moderate | 5 (10%) | 0 | |
Severe | 1 (2%) | 0 | |
Not available | 1 (2%) | 0 (0%) | |
Aortic stenosis | < 0.001 | ||
Mild or less | 23 (50%) | 50 (100%) | |
Moderate | 22 (48%) | 0 | |
Severe | 1 (2%) | 0 | |
Not available | 2 (4%) | 0 | |
β blocker and/or ARB use | 30 (61%) | 24 (48%) | 0.22 |