Variables | Healthy Controls (n = 75) | rTOF (n = 75) | PAH (n = 75) |
---|---|---|---|
Age, years | 37 ± 15 | 31 ± 12* | 37 ± 15# |
Gender, Male/Female | 16/59 | 39/36* | 16/59# |
Body surface area, m2 | 1.6 ± 0.2 | 1.7 ± 0.2 | 1.5 ± 0.2*# |
Diastolic blood pressure, mmHg | 74 ± 11 | 71 ± 9 | 71 ± 12 |
Systolic blood pressure, mmHg | 126 ± 18 | 121 ± 16 | 112 ± 19*# |
Heart rate, bpm | 76 ± 13 | 78 ± 15 | 85 ± 16*# |
WHO class (> 1), n (%) | 0 (0 %) | 4 (5.3 %) | 69 (92 %)*# |
CMR: left ventricle | |||
LVEDVI, ml/m2 | 70 ± 11 | 73 ± 17 | 72 ± 30 |
LVESVI, ml/m2 | 26 ± 7 | 30 ± 11* | 32 ± 17* |
LVSVI, ml/m2 | 44 ± 6 | 43 ± 9 | 41 ± 16 |
LVEF, % | 64 ± 6 | 59 ± 8* | 57 ± 10* |
LV mass index, g/m2 | 40 ± 10 | 48 ± 12* | 54 ± 19*# |
CMR: right ventricle | |||
RVEDVI, ml/m2 | 73 ± 13 | 142 ± 30* | 122 ± 59*# |
RVESVI, ml/m2 | 30 ± 10 | 77 ± 19* | 74 ± 46* |
RVSVI, ml/m2 | 42 ± 7 | 65 ± 16* | 48 ± 23# |
RVEF, % | 60 ± 7 | 46 ± 6* | 42 ± 14*# |
RV GCS, % | 12.0 ± 4.2 | 15.4 ± 5.2* | 11.0 ± 5.3# |
RV GLS, % | 29.6 ± 3.1 | 23.8 ± 3.0* | 20.4 ± 5.9*# |
RV GLSRs, 1/s | 1.5 ± 0.3 | 1.1 ± 0.2* | 1.1 ± 0.4* |
RV GLSRe, 1/s | 1.5 ± 0.4 | 1.4 ± 0.4 | 0.8 ± 0.4*# |
RV GLSRa, 1/s | 1.0 ± 0.4 | 0.6 ± 0.3* | 1.0 ± 0.5# |
RV fast GLS, % | 24.4 ± 3.0 | 19.3 ± 2.4* | 15.1 ± 4.9*# |
RV fast GLSRs, 1/s | 1.2 ± 0.3 | 0.9 ± 0.2* | 0.9 ± 0.3*# |
RV fast GLSRe, 1/s | 1.7 ± 0.4 | 1.4 ± 0.4* | 0.8 ± 0.4*# |
RV fast GLSRa, 1/s | 1.0 ± 0.3 | 0.6 ± 0.2* | 0.8 ± 0.4*# |