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Table 6 Kawasaki disease and systemic vasculitis

From: SCMR expert consensus statement for cardiovascular magnetic resonance of acquired and non-structural pediatric heart disease

Sequence

Imaging plane

Indication

Standard imaging

 2D Cine bSSFP

Short-axis stack

LV volumes, mass, and EF

RV volumes, mass, and EF

Regional wall motion

LV long axis views

 3D bSSFP respiratory-gated and ECG-triggered whole heart sequencea

3D Volume

Coronary artery assessment for aneurysm formation

 Non-ECG gated 3D magnetic resonance contrast angiography

3D Volume

Extracardiac vascular lumen imaging for detection of aneurysm formation

 Late gadolinium enhancement

Short-axis stack

LV long-axis views

RV-specific views

Myocardial scarring

Additional case-specific or comprehensive imaging

 Navigator gated 3D LGE [110, 111]

 

Coronary or large vessel wall enhancement in patients with systemic arterial inflammation

 T1 mapping

Short-axis stack

Acute myocardial inflammation (edema) or fibrosis

 T2 signal intensity ratio OR T2 mapping

Short-axis stack

Acute myocardial inflammation (edema)

 Rest and stress myocardial perfusion

Short-axis stack

Suspected coronary stenosis including microvascular disease of the myocardium

 Phase contrast flow

As indicated

KD-related decreased ventricular output or valve insufficiency

  1. 3D three dimensional, ECG electrocardiogram, EF ejection fraction, KD kawasaki disease, LV left ventricular, RV right ventricular, bSSFP balanced steady state free precession
  2. aImaging can be performed during systole or diastole according to patient age and heart rate