Table 1 Control and Duchenne muscular dystrophy-associated cardiomyopathy (DMD CMP) patient information

Age (years)

16.2 [13.3–20.7]

12.2 [10.7–16.5]*

15.7 [14.0–17.8]

10.6 [8.7–11.7]*

12.9 [11.2–16.0]*

17.4 [ 14.0–19.1]

Height (cm)

170 [160–185]

147 [132–160]*

158 [152–168]*

127 [122–142.5]*

152 [145–157.75]*

163 [145–170]*

Weight (kg)

67.0 [54.9–81.4]

49.1 [37.5–65.2]*

58.2 [49.5–72.0]

38.6 [31.9–57.8]*

52.3 [45.9–62.1]

55.7 [42.7–64.5]

LVEF (%)

61.0 [57.8–64.3]

59.0 [53.0 – 62.0]*

56.0 [49.0 – 60.0]*

62.0 [59.5 – 64.0]

59.0 [58.5–60.5]

49.0 [47.0 – 52.0]*

LVEF < 55%, n (%)

0 (0)

13 (30.23)

11 (44)

0 (0)

0 (0)

13 (100)

LVEDVI (%)

82 [73–90]

60 [55–73]*

60 [56–73]*

57 [53–66]*

59 [56–62]*

73 [68–83]

LVESVI (%)

55 [40–69]

25 [22–35]*

25 [23–37]

22 [19–25]*

25 [23–26]*

37 [34–50]*

LV CO (L/min)

5.5 [5.1–7.1]†

4.9 [4.1–5.9]*

5.2 [4.2–6.2]

4.5 [3.9–5.7]*

4.9 [ 4.4–5.7]*

5.2 [4.6–6.2]

 + LGE, n (%)

0 (0)†

28 (65)

20 (80)

0 (0)

15 (100)

13 (100)

Systolic BP (mmHg)

125 [112–132]†

114 [107 -118]

114 [107–118]

116 [107–122]

115 [112–115.5]

108 [103–115]

Diastolic BP (mmHg)

57 [54–57]†

66 [63–74]*

68 [63–75]*

64 [63–72]

70 [65–75]*

66 [60–69]

HR (BPM)

75 [68–91]†

99 [92–110]*

98 [84–110]*

102 [96–118]*

98 [89–104]*

101 [90–109]

BSA (m²)

1.74 [1.60–1.99]†

1.45 [1.19–1.68]*

1.58 [1.46–1.84]

1.19 [1.07–1.465]*

1.50 [1.37–1.66]*

1.50 [1.43–1.75]