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Table 2 Echocardiographic parameters in patients with Miyoshi myopathy

From: Early detection of cardiac involvement in Miyoshi myopathy: 2D strain echocardiography and late gadolinium enhancement cardiovascular magnetic resonance

  #1 #2 #3 #4 #5
LVEDD (mm) 50 54 47 56 41
LVESD (mm) 30 31 30 44 25
Ejection Fraction (%) 64 67 59 45 63
E velocity (m/sec) 0.91 0.89 0.80 0.42 0.64
A velocity (m/sec) 0.54 0.51 0.60 0.61 0.66
E/A ratio (m/sec) 1.69 1.75 1.33 0.69 0.97
E' velocity (m/sec) 0.11 0.10 0.09 0.05 0.073
E/E' ratio 8.27 8.9 8.89 8.40 8.77
RWMA (-) (-) (-) Hypokinesia of basal and mid inferior wall (-)
Global PSLS (%) -15.7 -20.9 -17.4 -16.8 -23.4
PSLS at long-axis view (%) -12.8 -19.3 -17.1 -17.0 -24.6
PSLS at 4-chamber view (%) -16.8 -20.9 -18.9 -16.0 -22.7
PSLS at 2-chamber view (%) -17.4 -22.7 -16.2 -17.3 -22.9
Segmental PSLS      
Basal Anterior -22 -15 -24 -15 -22
   AS -15 -18 -16 -13 -18
   IS -17 -18 -16 -12 -18
   Inferior -17 -18 -23 -9 -25
   IL 4 -17 -19 -14 -25
   AL -18 -11 -20 -12 -26
Mid Anterior -14 -13 -24 -17 -22
   AS -18 -19 -17 -22 -25
   IS -19 -18 -18 -15 -21
   Inferior -19 -19 -21 -12 -24
   IL -11 -15 -21 -13 -25
   AL -15 -9 -21 -19 -22
Apical anterior -15 -16 -21 -23 -25
   septum -20 -21 -23 -25 -28
   Inferior -20 -29 -22 -18 -25
   lateral -15 -17 -23 -25 -24
Apical cap -17 -18 -22 -23 -26
  1. LVEDD = left ventricular end-diastolic diameter, LVESD = left ventricular end-systolic diameter, E = peak transmitral flow velocity during early diastole, A = peak transmitral flow velocity during late diastole, E'= peak mitral annular velocity during early diastole, RWMA = regional wall motion abnormality, PSLS = peak systolic longitudinal strain, AS = anteriorseptum, IS = inferiorseptum, IL = inferiorlateral, AL = anteriorlateral.