Table 2 Echocardiographic parameters in patients with Miyoshi myopathy
| Â | #1 | #2 | #3 | #4 | #5 |
|---|---|---|---|---|---|
LVEDD (mm) | 50 | 54 | 47 | 56 | 41 |
LVESD (mm) | 30 | 31 | 30 | 44 | 25 |
Ejection Fraction (%) | 64 | 67 | 59 | 45 | 63 |
E velocity (m/sec) | 0.91 | 0.89 | 0.80 | 0.42 | 0.64 |
A velocity (m/sec) | 0.54 | 0.51 | 0.60 | 0.61 | 0.66 |
E/A ratio (m/sec) | 1.69 | 1.75 | 1.33 | 0.69 | 0.97 |
E' velocity (m/sec) | 0.11 | 0.10 | 0.09 | 0.05 | 0.073 |
E/E' ratio | 8.27 | 8.9 | 8.89 | 8.40 | 8.77 |
RWMA | (-) | (-) | (-) | Hypokinesia of basal and mid inferior wall | (-) |
Global PSLS (%) | -15.7 | -20.9 | -17.4 | -16.8 | -23.4 |
PSLS at long-axis view (%) | -12.8 | -19.3 | -17.1 | -17.0 | -24.6 |
PSLS at 4-chamber view (%) | -16.8 | -20.9 | -18.9 | -16.0 | -22.7 |
PSLS at 2-chamber view (%) | -17.4 | -22.7 | -16.2 | -17.3 | -22.9 |
Segmental PSLS | Â | Â | Â | Â | Â |
Basal Anterior | -22 | -15 | -24 | -15 | -22 |
   AS | -15 | -18 | -16 | -13 | -18 |
   IS | -17 | -18 | -16 | -12 | -18 |
   Inferior | -17 | -18 | -23 | -9 | -25 |
   IL | 4 | -17 | -19 | -14 | -25 |
   AL | -18 | -11 | -20 | -12 | -26 |
Mid Anterior | -14 | -13 | -24 | -17 | -22 |
   AS | -18 | -19 | -17 | -22 | -25 |
   IS | -19 | -18 | -18 | -15 | -21 |
   Inferior | -19 | -19 | -21 | -12 | -24 |
   IL | -11 | -15 | -21 | -13 | -25 |
   AL | -15 | -9 | -21 | -19 | -22 |
Apical anterior | -15 | -16 | -21 | -23 | -25 |
   septum | -20 | -21 | -23 | -25 | -28 |
   Inferior | -20 | -29 | -22 | -18 | -25 |
   lateral | -15 | -17 | -23 | -25 | -24 |
Apical cap | -17 | -18 | -22 | -23 | -26 |