Table 1
From: MRI assessment of left ventricular structure and function in children with infantile Pompe disease
Subject | Sex | Age(m) at start of ERT | Months post-ERT | MRI Sedation | MRI Technique | LVM (gm/m2) | LV EF | Delayed Enhancement |
|---|---|---|---|---|---|---|---|---|
1 | F | 4 | 7 | No | Cine-TrueFISP | 135 | 25% | No |
1 | Â | Â | 9 | No | Real-Time | 180.6 | 58% | No |
1 | Â | Â | 13 | No | Real-Time | 179.6 | 55% | No |
2 | M | 7 | 15 | No | Real-Time | 51.2 | 55% | No |
2 | Â | Â | 26 | No | Real-Time | 57 | 57% | No |
2 | Â | Â | 47 | Yes | Both | 44.5 | 68% | No |
3 | M | 6 | 1 | No | Real-Time | 334 | 18% | No |
3 | Â | Â | 2 | No | Real-Time | 303 | 25% | No |
4 | M | 3 | 6 | No | Real-Time | 43.8 | 55% | No |
4 | Â | Â | 36 | Yes | Real-Time | 43 | 69% | No |
5 | M | 1 | 0 | No | Real-Time | 94 | 73% | No |
5 | Â | Â | 20 | Yes | Both | 34 | 57% | No |
6 | M | 4 | 34 | No | Cine-TrueFISP | 47.0 | 60% | No |
7 | M | 6 | 2 | No | Cine-TrueFISP | 252.2 | 65% | No |
8 | M | 4 | 3 | No | Real-Time | 180.6 | 29% | No |
9 | F | 10 | 1 | No | Real-Time | 324.4 | 55% | No |
10 | M | 3 | 31 | Yes | Both | 145.0 | 73% | Yes |