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Table 1

From: MRI assessment of left ventricular structure and function in children with infantile Pompe disease

Subject Sex Age(m) at start of ERT Months post-ERT MRI Sedation MRI Technique LVM (gm/m2) LV EF Delayed Enhancement
1 F 4 7 No Cine-TrueFISP 135 25% No
1    9 No Real-Time 180.6 58% No
1    13 No Real-Time 179.6 55% No
2 M 7 15 No Real-Time 51.2 55% No
2    26 No Real-Time 57 57% No
2    47 Yes Both 44.5 68% No
3 M 6 1 No Real-Time 334 18% No
3    2 No Real-Time 303 25% No
4 M 3 6 No Real-Time 43.8 55% No
4    36 Yes Real-Time 43 69% No
5 M 1 0 No Real-Time 94 73% No
5    20 Yes Both 34 57% No
6 M 4 34 No Cine-TrueFISP 47.0 60% No
7 M 6 2 No Cine-TrueFISP 252.2 65% No
8 M 4 3 No Real-Time 180.6 29% No
9 F 10 1 No Real-Time 324.4 55% No
10 M 3 31 Yes Both 145.0 73% Yes