Cardiovascular Magnetic Resonance in Marfan syndrome

Table 5 European guidelines for imaging in MFS

Diagnostic	Follow-up
TTE of aortic root: measure at annulus, sinuses of Valsalva, sinotubular junction and distal ascending aorta.	TTE on an annual basis if stable
TTE of left ventricular and valvular function.	TTE on an annual basis if stable
Either CMR or CT of entire aorta *	CMR or CT of entire aorta: every 5 yr if normal aortic dimensions beyond root; at least annually if aneurysm formation beyond root.
Avoid coronary angiography due to increased dissection risk
CT coronary angiography pre-op to assess for coronary disease where possible
TOE- only in assessment of suspected aortic dissection

*CMR assessment of aortic wall biophysical properties may be possible – see CMR section below.

ISSN: 1532-429X