All patients | RV myocardial enhancement | No RV myocardial enhancement | P | |
---|---|---|---|---|
N = 30 | N = 21 | N = 9 | ||
Age at baseline (years) | 43.4 ± 13 | 43.4 ± 11.4 | 43.3 ± 17.8 | 0.99 |
Oxygen saturation (%) | 81 ± 7 | 81 ± 7 | 81 ± 6 | 0.78 |
Female | 20 (67%) | 14 (67%) | 6 (67%) | 0.99 |
History of arrhythmia | 3 (10%) | 2 (9%) | 1 (11%) | 0.60 |
Hemoglobin (g/dl) | 20 ± 2.6 | 20.3 ± 2.8 | 19.3 ± 2.1 | 0.34 |
Creatinine (μmol/l) | 86 ± 24.6 | 86 ± 24 | 88 ± 28 | 0.81 |
Urea (mmol/l) | 6.1 ± 2.8 | 5.9 ± 2.3 | 6.3 ± 3.5 | 0.75 |
Brain natriuretic peptide (pmol/l)* | 15/14 | 14/24 | 15/13 | 0.99 |
RV ejection fraction (%) | 51 ± 14 | 51 ± 13 | 50 ± 18 | 0.69 |
LV ejection fraction (%) | 57 ± 11 | 59 ± 10 | 51 ± 12 | 0.06 |
PACO2 (kPa) | 4.4 ± 0.7 | 4.5 ± 0.6 | 4.1 ± 0.8 | 0.35 |
PAO2 (kPa) | 6.4 ± 0.9 | 6.4 ± 0.9 | 6.4 ± 0.9 | 0.93 |
Exercise Duration (min) | 5.7 ± 2.4 | 5.2 ± 2.1 | 6.2 ± 2.8 | 0.30 |
VO2 at peak (ml/kg/min) | 11.1 ± 3.9 | 10.7 ± 3.5 | 11.9 ± 4.8 | 0.46 |
VE/CO2slope | 87 ± 69 | 96 ± 82 | 66 ± 18 | 0.29 |
% predicted peak VO2 | 36 ± 11 | 35 ± 11 | 36 ± 13 | 0.70 |
6 minute walk distance (m) | 388 ± 108 | 405 ± 110 | 348 ± 96 | 0.19 |
Death during follow up (yr) | 7 (23%) | 4 (19%) | 3 (33%) | 0.13 |