Fig. 2

A 48-year-old male patient with PRKAG2 cardiac syndrome and a pacemaker. In short-axis and four chamber cine images septum is severely hypertrophied (a-b) (black arrows). Maximal septal and lateral wall thickness was 31 mm and 25 mm, respectively. Papillary muscles were excluded in the measurements. Anteroseptal, hypertrophic areas exhibit patchy late gadolinium enhancement (c-d) (white arrows). White arrow heads indicate artefact from pacemaker lead