From: Cardiovascular magnetic resonance findings in patients with PRKAG2 gene mutations
Segment | |||||||
---|---|---|---|---|---|---|---|
Anterior | Anteroseptal | Inferoseptal | Inferior | Inferolateral | Anterolateral | Mean | |
Native T1 values | |||||||
Family 1 (n = 5) | |||||||
R302Q mutation (n = 4) | |||||||
LGE negative (n = 3) | |||||||
1 | 934 | 932 | 944 | 905 | 897 | 929 | 924 |
2 | 914 | 902 | 925 | 924 | 879 | 894 | 906 |
3 | 922 | 938 | 945 | 919 | 905 | 918 | 925 |
Mean | 923 | 924 | 938 | 916 | 894 | 914 | 918 |
LGE positive (n = 1) | m. v. | m. v. | 990 | 944 | 986 | m. v. | 973 |
No mutation (n = 1) | 984 | 954 | 938 | 960 | 984 | 955 | 963 |
Family 2 (n = 1) | |||||||
H344P mutation (n = 1) | 950 | 965 | 985 | 968 | 957 | 969 | 966 |
Native T2 values | |||||||
Family 1 (n = 5) | |||||||
R302Q mutation (n = 4) | |||||||
LGE negative (n = 3) | |||||||
1 | 42.8 | 44.4 | 39.9 | 39.7 | 43.9 | 40.5 | 41.9 |
2 | 41.4 | 44.3 | 43.8 | 43.0 | 43.2 | 40.3 | 42.7 |
3 | 42.1 | 46.5 | 42.2 | 40.5 | 45.5 | 40.2 | 42.8 |
Mean | 42.1 | 45.1 | 42.0 | 41.1 | 44.2 | 40.3 | 42.5 |
LGE positive (n = 1) | m. v. | m. v. | 41.9 | 40.2 | 39.9 | m. v. | 40.7 |
No mutation (n = 1) | 43.3 | 47.6 | 41.5 | 37.2 | 43.2 | 39.0 | 42.0 |
Family 2 (n = 1) | |||||||
H344P mutation (n = 1) | 50.4 | 50.0 | 49.0 | 45.4 | 50.4 | 45.4 | 48.4 |