Myocardial fibrosis by late gadolinium enhancement cardiovascular magnetic resonance in myotonic muscular dystrophy type 1: highly prevalent but not associated with surface conduction abnormality

Table 2 Characteristics of Subjects with MMD undergoing PPM implant

#	Age (years)	Sex	Disease Length (years)	NYHA Class	MIRS Scale	LVEDVI, (ml/m²)	LVESVI, (ml/m²)	LVEF, (%)	LGE Any	LGE (%)	ECV (%)	Rhythm	HR (bpm)	PR (ms)	QRS (ms)	QTc	Surface Conduction Disease	AV block type	LAFB	LBBB	RBBB	IVCD	Bif. Block	HV (ms)	HV > 70 ms
1	48	F	28	3	2	65.8	29.5	55.2	0	0	27.5	sinus	62	220	186	519	1	I	0	1	0	0	0	73	1
2	36	M	28	1	5	87.0	38.5	55.7	0	0	22.4	sinus	54	236	116	402	1	I	0	0	0	1	0	77	1
3	44	M	5	1	3	78.6	36.2	53.9	1	2.7	26.2	Mobitz 1	35	440	102	366	1	II	0	0	0	0	0	N/A	N/A
4	31	F	9	2	4	73.3	29.3	60.0	0	0	26.8	sinus	103	220	86	466	1	I	1	0	0	0	0	N/A	N/A
5	42	F	5	1	4	63.9	32.2	49.6	0	0	33.8	sinus	74	220	116	477	1	I	1	0	0	1	0	86	1
6	34	F	12	1	3	61.1	35.3	42.2	1	5.4	27.2	sinus	70	210	112	481	1	I	0	0	0	1	0	N/A	N/A
7	61	F	12	2	5	46.8	20.0	57.3	0	0	21.7	sinus	74	220	118	463	1	I	0	0	0	1	0	N/A	N/A
8	53	M	36	1	3	50.0	15.6	68.8	1	13.7	21.2	sinus	54	250	132	411	1	I	0	1	0	0	0	95	1
9	55	M	1	1	3	43.5	12.0	72.4	1	16.2	24.3	sinus	61	220	142	446	1	I	0	0	1	0	0	71	1
10	48	F	30	2	3	76.3	26.8	64.8	0	0	31.8	sinus	49	236	120	419	1	I	1	0	0	1	1	N/A	N/A
11	40	F	1	2	4	61.0	28.8	53.3	1	11.8	25.4	sinus	80	156	132	452	1	None	1	0	0	0	0	75	1
12	43	F	14	1	3	73.2	27.5	62.5	0	0	29.9	sinus	68	150	142	472	1	None	1	0	1	0	1	80	1
13	33	M	8	2	3	70.5	32.4	54.0	0	0	25.0	sinus	68	240	84	421	1	I	0	0	0	0	0	N/A	N/A
14	31	F	26	2	3	64.8	27.2	58.1	0	0	23.4	sinus	83	205	128	434	1	I	1	0	1	0	1	74	1
15	26	M	18	2	3	57.7	24.4	57.7	1	5.1	20.7	sinus	98	205	96	439	1	I	1	0	1	0	1	72	1

LVEDVI left ventricular end-diastolic volume index, LVESVI left ventricular end-systolic volume index, LVEF left ventricular ejection fraction, LGE late gadolinium enhancement, ECV extracellular volume fraction, HR heart rate, LAFB left anterior fascicular block, LBBB left bundle branch block, RBBB right bundle branch block, IVCD nonspecific intraventricular conduction delay, Bif. block bifascicular block, HV His-Ventricular interval

ISSN: 1532-429X