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Table 1 Patients with multiple sources of pulmonary blood flow. MRI Cardiac Catheter allows for the measurement of pulmonary vascular resistance in patients with complex congenital heart disease. Differential pulmonary vascular resistance can be measured when there are multiple sources of pulmonary blood flow.

From: 209 MRI cardiac catheter assessment of total and differential pulmonary vascular resistance in the context of single ventricle physiology

  Age (years) Diagnosis Procedures Sources of pulmonary blood flow PVR (WU.m2) Outcome
      Right Left Total  
1 3.1 Right atrial isomerism Complete atrioventricular septal defect Double outlet right ventricle Recurrent chylothoraces TCPC SVC and IVC 4.4 3.6 2.0 Conservative management of chylothoarces
2 3.0 Hypoplastic Left Heart Syndrome Recurrent ascites TCPC SVC and IVC 6.8 5.0 2.9 Recreation of atrial fenestration
3 12.5 Double inlet left ventricle Transposition Great Arteries Hypoplastic right ventricle SCPC SVC MPA 3.3 4.3 1.9 Proceed to TCPC
4 11.5 Right atrial isomerism Atrioventricular Septal Defect Pulmonary atresia Protein losing enteropathy TCPC SVC and IVC 9.3 1.9 1.6 Medical treatment of protein losing enteropathy
5 13.7 Mitral valve dysplasia Hypoplastic left ventricle Double outlet right ventricle PA Band MPA Right MBTS 6.9 2.7 1.9 Proceed to SCPC
6 1.47 Pulmonary atresia intact ventricular septum Pulmonary valvotomy and ductal stent MPA Arterial duct 6.0 3.3 2.1 Proceed to SCPC
7 41.7 Situs inversus Double inlet left ventricle Atrioventricular septal defect Pulmonary stenosis Right MBTS Pulmonary valvotomy MPA Right MBTS 5.5 3.2 2.0 Suitable for SCPC, patient elected for conservative management
  1. Abbreviations: TCPC – Total cavo-pulmonary connection, SVC – superior vena cava, IVC – inferior vena cava, MPA – Main Pulmonary Artery, SCPC – Superior cavo-pulmonary connection, MBTS – Modified Blalock Taussig shunt.