Table 1 Patients with multiple sources of pulmonary blood flow. MRI Cardiac Catheter allows for the measurement of pulmonary vascular resistance in patients with complex congenital heart disease. Differential pulmonary vascular resistance can be measured when there are multiple sources of pulmonary blood flow.
| Â | Age (years) | Diagnosis | Procedures | Sources of pulmonary blood flow | PVR (WU.m2) | Outcome | ||
|---|---|---|---|---|---|---|---|---|
| Â | Â | Â | Â | Â | Right | Left | Total | Â |
1 | 3.1 | Right atrial isomerism Complete atrioventricular septal defect Double outlet right ventricle Recurrent chylothoraces | TCPC | SVC and IVC | 4.4 | 3.6 | 2.0 | Conservative management of chylothoarces |
2 | 3.0 | Hypoplastic Left Heart Syndrome Recurrent ascites | TCPC | SVC and IVC | 6.8 | 5.0 | 2.9 | Recreation of atrial fenestration |
3 | 12.5 | Double inlet left ventricle Transposition Great Arteries Hypoplastic right ventricle | SCPC | SVC MPA | 3.3 | 4.3 | 1.9 | Proceed to TCPC |
4 | 11.5 | Right atrial isomerism Atrioventricular Septal Defect Pulmonary atresia Protein losing enteropathy | TCPC | SVC and IVC | 9.3 | 1.9 | 1.6 | Medical treatment of protein losing enteropathy |
5 | 13.7 | Mitral valve dysplasia Hypoplastic left ventricle Double outlet right ventricle | PA Band | MPA Right MBTS | 6.9 | 2.7 | 1.9 | Proceed to SCPC |
6 | 1.47 | Pulmonary atresia intact ventricular septum | Pulmonary valvotomy and ductal stent | MPA Arterial duct | 6.0 | 3.3 | 2.1 | Proceed to SCPC |
7 | 41.7 | Situs inversus Double inlet left ventricle Atrioventricular septal defect Pulmonary stenosis | Right MBTS Pulmonary valvotomy | MPA Right MBTS | 5.5 | 3.2 | 2.0 | Suitable for SCPC, patient elected for conservative management |