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  • Open Access

Cardiovascular magnetic resonance imaging findings in Ebstein anomaly

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Journal of Cardiovascular Magnetic Resonance201214 (Suppl 1) :P107

https://doi.org/10.1186/1532-429X-14-S1-P107

  • Published:

Keywords

  • Congenital Heart Disease
  • Cardiovascular Magnetic Resonance
  • Cardiac Magnetic Resonance
  • Tricuspid Valve
  • Cardiac Magnetic Resonance Imaging

Background

In recent years, cardiac magnetic resonance (CMR) imaging has emerged as the reference standard for cardiac imaging in patients with many forms of congenital heart disease, in particular for lesions that affect the right ventricle. Few studies have been published in assessment of Ebstein anomaly by CMR imaging.

Methods

CMR studies of patients with EA conducted from June 2007 to June 2011 were analized. Cine spin echo images in multiple views, and angiography were evaluated to assess chambers morphology and diameters, wall thickness and left ventricular function, also were measured the atrialized right ventricular portion and the functional tricuspid valve position. And Inversion Recovery sequence for determination of fibrosis.

Results

Ninety four patients were studied. Table 1 summarizes the main results. Tricuspid valve regurgitation was found in 96.9%, severe in 62. 5% of the cases. The presence of left ventricle fibrosis was significant associated with right ventricle longest dimension including the atrialized portion (p=0.003), the diastolic and systolic diameters (p=0.011 and p=0.005).
Table 1

Results

Variable

Mean

SD

Age (years)

23.0

13.02231

LVdV (mm)

36.5

8.36997

LVsD (mm)

25.7

6.55335

dS (mm)

7.9

10.5891

Lateral wall diastolic (mm)

6.2

1.42729

RVdD (mm)

55.6

20.61004

RVsD (mm)

47.6

21.16745

Right ventricular longitudinal diameter (mm)

96.1

22.96363

RVfw (mm)

4.5

1.40918

RA U/L (mm)

66.0

22.36908

RA M/L (mm)

63.9

20.99671

LA U/L (mm)

44.1

16.28296

LA M/L

36.6

14.03464

LVEF (%)

47.2

10.96851

LV mass (gr)

60.0

28.60894

LVEDV (ml)

78.1

34.64511

LVESV (ml)

40.7

18.73527

Left ventricular stroke volume (ml)

36.6

19.18734

Atrialized portion of right ventricle (mm)

56.1

26.3945

Atrialized portion of right ventricle (%)

59.3

19.84599

Atrial septal defect (mm)

5.7

6.98696

Pulmonary artery (mm)

19.6

6.87248

Right pulmonary branch (mm)

12.8

4.50256

Left pulmonary branch (mm)

13.3

4.49312

LVdD: Left ventricular diastolic diameter; LVsD: Left ventricular systolic diameter; dS: diastolic septum; RVdD: right ventricular diastolic diameter; RVsD: right ventricular systolic diameter; RVfw: right ventricular free Wall; RA U/L: right atrium upper/lower; RA M/L: right atrium mid/lateral; LA U/L: left atrium upper/lower; LA M/L: mid/lateral; LVEF: ejection fraction; LV: left ventricular; LVEDVI: end-diastolic volume; LVESVI: end-systolic volume.

Conclusions

CMR findings in EA were demonstrated. There was a clear positive relationship between the presence of LV fibrosis and the right ventricle dimensions.

Funding

National Institute of Cardiology "Ignacio Chávez", Mexico City, Mexico.

Authors’ Affiliations

(1)
Cardiovascular Magnetic Resonance Imaging, National Institute of Cardiology "Ignacio Chávez", Mexico City, Mexico
(2)
Embryology, National Institute of Cardiology "Ignacio Chávez", Mexico City, Mexico
(3)
Nuclear Cardiology, National Institute of Cardiology "Ignacio Chávez", Mexico City, Mexico

Copyright

© González et al; licensee BioMed Central Ltd. 2012

This article is published under license to BioMed Central Ltd. This is an open access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

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